ACY1 Monoclonal Antibody (Clone AT1E2)

氨基酰化酶1单克隆抗体

Aminoacylase-1, also designated N-acyl-L-amino-acid amidohydrolase or ACY1, is a member of the largest metallopeptidase family called M20A. Aminoacylase-1 is a zinc-binding homodimeric enzyme expressed in kidney, brain, placenta and spleen. It is the most abundant of the aminoacylases. Defects in ACY1 are the cause of aminoacylase-1 deficiency (ACY1D). ACY1D results in a metabolic disorder manifesting with encephalopathy, unspecific psychomotor delay, psychomotor delay with atrophy of the vermis and syringomyelia, marked muscular hypotonia or normal clinical features. All affected individuals exhibit markedly increased urinary excretion of several N-acetylated amino acids.
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基本信息

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货号 MA01011
规格 100 µL
宿主 Mouse
免疫原 Recombinant human ACY1 (1-408aa) purified from E. coli
特异性
亚型 IgG2b,k
反应性 Human
克隆 Anti-human ACY1 mAb, clone AT1E2, is derived from hybridization of mouse F0 myeloma cells with spleen cells from BALB/c mice immunized with a recombinant human ACY1 protein.
Uniprot
浓度 1 mg/mL
推荐稀释度
配方 Liquid. In Phosphate-Buffered Saline (pH 7.4) with 0.02% Sodium Azide, 10% Glycerol.
应用范围 ELISA, WB, Flow cytometry, ICC/IF
别名 ACY1D, ACYLASE, Aminoacylase 1.
保存条件 冻干产品: 2 - 8°C保存5年; 液体: -20°C保存2年.
注意 仅用于科学研究, 不能用于疾病诊断.

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